Congenital absence of the...

A hospital's fertility centre received a referral for a 31-year-old infertile lady. The patient stated that she had been diagnosed with congenital absence of the uterus and ovaries at the age of 16 years after being checked for primary amenorrhea. She already had adrenarche and thelarche, along with a linear growth spurt when she was 12 years old. The absence of the uterus and cervix was confirmed by ultrasound of the pelvis. There were several simple cyst clusters in the adnexal region on the right side (one measuring 24 mm by 25 mm and another measuring 18 mm by 17 mm), as well as on the left side (one measuring 18 mm by 17 mm and another measuring 20 mm by 21 mm). The right ovary was not visible. A normal-length vagina was visible on an MRI of the pelvis that was done both before and after the administration of contrast material (Figure ). There was no evident uterus or cervix found. Following the anticipated path of the round ligaments of the uterus, cordlike structures, which were most visible in the contrast-enhanced pictures, extended from the superior portion of the vagina to the right and left inguinal canals.