An exceptional case of bl...

Bladder exstrophy is a rare birth defect in which the anterior wall of the abdomen over the bladder is not closed in the intrauterine period, hence the child is born with an exposed bladder. The incidence of bladder exstrophy is 1/10,000 childbirths. Complaints would vary from exposed bladder, incontinence or leakage of urine, defects in genitals and pelvic bones as well as defects in intestine and reproductive organs. Most patient get operated on with bladder exstrophy repair in infant age. If it gets neglected, it needs stage-wise surgery in this case. Parents of a 3-year-old male child came to a Paediatric surgeon OPD with congenital bladder exstrophy. Orthopaedic surgeons´ opinion was taken in view of pubic diastasis. In infant age, there is no need for additional concern of pubic diastasis. At the age of 3 acetabulo-pelvic surgeon advised for External fixator application of pelvic wings to decrease tension on reconstructed bladder wall and inter-pubic ligament. The patient managed as neglected bladder exstrophy. Reconstruction of abdominal wall and urethra reconstruction done and application of external fixator application done.

Ref: Rahul Agola et al. An exceptional case of bladder exstrophy with pubic symphysis diastasis in a 3-year-old male child. PAMJ - Clinical Medicine. 2023;11:21. [doi: 10.11604/pamj-cm.2023.11.21.38640]